| 摘要: |
| 特发性肺纤维化(idiopathic pulmonary fibrosis,IPF)患者病程中出现的突然的、不可预测的临床急剧恶化称为特发性肺纤维化急性加重(acute exacerbations of idiopathic pulmonary fibrosis以下称为AE-IPF)。其病情凶险,病死率高,且临床并非少见。目前AE-IPF病因、机制未明,现有的诊断标准尚有争议,缺乏有效的治疗措施,是临床医生面临的诊治难点之一。 |
| 关键词: 特发性肺纤维化 急性加重 感染 诊断 治疗 |
| DOI：10.3969/j.issn1008-0392.2012.04.025 |
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| 基金项目:国家自然科学基金（30971323) |
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| Current progress in acute exacerbations of idiopathic pulmonary fibrosis |
| MA Zhao-juan,LI Hui-ping |
| () |
| Abstract: |
| Acute exacerbations of idiopathic pulmonary fibrosis (AE4PF) is a sudden，unpredictable clinical deterioration， which emerges in the course of idiopathic pulmonary fibrosis. It is a serious disease with high mortality and not uncommon in clinical practice. So far， the etiology and pathogenesis of AE-IPF is unclear. The existing diagnostic criteria of AE-IPF are controversial and there is still lack of effective Methods for treatment of AE-IPF. |
| Key words: idiopathic pulmonary fibrosis acute exacerbation infection diagnosis treatment |
